Patients with phenylketonuria indicated interruptions in special nutrition

Patients with phenylketonuria have experienced interruptions in the delivery of amino acid mixtures in eight regions, the All-Russian Society of Phenylketonuria told Izvestia. Problems with their issuance were recorded in the Nizhny Novgorod, Chelyabinsk, Vologda, Samara regions, as well as in Moscow, Bashkiria, Chuvashia and the Krasnoyarsk Territory.

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So, in Bashkiria, doctors stopped prescribing amino acid mixtures to minors with phenylketonuria back in the fall of 2024, but at first they began to give out a much smaller amount than before.

"Instead of 33 cans, patients were then given only three to six packs each, and then stopped. Then, patients in the republic were given food again, but it did not last long — in March 2025, interruptions began again," Almira Murdasheva, chairman of the regional public organization Phenylketonuria Bashkortostan, told Izvestia.

The main principle of phenylketonuria treatment is a strict diet with the exclusion of foods with a high content of phenylalanine from the diet, recalled Zarema Sakhtaryok, head of the medical and genetic consultation at the Maikop City Clinical Hospital.

"Such patients should not eat meat and fish in the first place, where this substance is most abundant," she added.

Valentin Denchik, a neurologist at Medline Service, emphasized that the accumulation of phenylalanine in patients with phenylketonuria can negatively affect IQ levels and lead to the development of mental retardation.

Read more in the exclusive Izvestia article:

Food sold out: patients with phenylketonuria are not given food